Bilateral linear nevus comedonicus on eyelids - A rare presentation

Naevus Comedonicus (NC) is an uncommon developmental defect of the pilosebaceous apparatus (or rarely, may be of the sweat duct) characterised by group of slightly elevated papules which have central, dark, firm hyperkeratosis plug resembling a comedo [1]. It was first described by Kofmann in 1895 [2]. It commonly affects scalp, face, trunk and uncommonly the genitalia [3], palms and soles [4]. Usually it is unilateral and an isolated cutaneous defect. Widespread cutaneous involvement or giant lesions are exceptional as are the systemic associations such as skeletal defects, cataract, cerebral anomalies [1,5,6] and arterio-hepatic dysplasias (Alagille syndrome) [7].